LCH disease and is the most severe form. Prevalence is estimated at 1:500,000 rosai dorfman disease pdf the disease almost exclusively occurs in children less than three years old. The name is derived from the names of Erich Letterer and Sture Siwe.
Letterer-Siwe is characterized by skin lesions, ear drainage, lymphadenopathy, osteolytic lesions, and hepatosplenomegaly. The skin lesions are scaly and may involve the scalp, ear canals, and abdomen. You can help by adding to it. You can help by adding to it.
The development of thrombocytopenia is a poor prognostic sign. Langerhans Cell Histiocytosis – Hematology and Oncology – Merck Manuals Professional Edition”.
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